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Anaesthetic considerations in progressive familial intrahepatic cholestasis (Byler's disease).

Bibliographic reference Müller, G ; Veyckemans, Francis ; Calier, M. ; Van Obbergh, L J ; De Kock, Marc ; et. al. Anaesthetic considerations in progressive familial intrahepatic cholestasis (Byler's disease).. In: Canadian journal of anaesthesia = Journal canadien d'anesthésie, Vol. 42, no. 12, p. 1126-33 (1995)
Permanent URL http://hdl.handle.net/2078.1/22505
  1. Linarelli LG, Williams CN, Phillips MJ. Byler’s disease: fatal intrahepatic cholestasis. J Pediatr 1972; 81: 484–92.
  2. Riely CA. Familial intrahepatic cholestatic syndromes. Semin Liver Dis 1987; 7: 119–33.
  3. Odièvre M, Hadchouel M, Landrieu P, Alagille D, Eliot N. Long-term prognosis for infants with intrahepatic cholestasis and patent extrahepatic biliary tract. Arch Dis Child 1981; 56: 373–6.
  4. Soubrane O, Gauthier F, DeVictor D, et al. Orthotopic liver transplantation for Byler’s disease. Transplantation 1990; 50: 804–6.
  5. Otte J-B, de Ville de Goyet J, Reding R, et al. Liver transplantation in children. In: Buts J-P, Sokal EM (Eds.). Management of Digestive and Liver Disorders in Infants and Children. Amsterdam: Elsevier, 1993; 669–77.
  6. Cartier M, van Obbergh L, Veyckemans F, et al. Intraoperative hemodynamic modifications during pediatric orthotopic liver transplantation. Intensive Care Med 1989; 15: S73–5.
  7. Clayton Robert J., Iber Frank L., Ruebner Boris H., McKusick Victor A., Byler's disease: Fatal familial intrahepatic cholestasis in an Amish kindred, 10.1016/s0022-3476(65)82107-2
  8. Jacquemin E, Dumont M, Bernard O, Erlinger S, Hadchouel M. Evidence for defective primary bile acid secretion in children with progressive familial intrahepatic cholestasis (Byler disease). Eur J Pediatr 1994; 153: 424–8.
  9. Whitington PF, Freese DK, Alonso EM, Schwarzenberg SJ, Sharp HL. Clinical and biochemical findings in progressive familial intrahepatic cholestasis. J Pediatr Gastroenterol Nutr 1994; 18: 134–41.
  10. Sokal EM. Nutritional and medical care in chronic cholestasis. In: Buts J-P, Sokal EM (Eds.). Management of Digestive Liver Disorders in Infants and Children. Amsterdam: Elsevier, 1993; 537–42.
  11. Barbé T, Losay J, Grimon G, et al. Pulmonary arteriovenous shunting in children with liver disease. J Pediatr 1995; 126: 571–9.
  12. Jacquemin E, Setchell KDR, O’Connell NC, et al. A new cause of progressive intrahepatic cholestasis: 3 β-hydroxy-C27-steroid dehydrogenase/isomerase deficiency. J Pediatr 1994; 125: 379–84.
  13. Lachaux A, Loras-Duclaux I, Bouvier R, Dumontet C, Hermier M. Benign recurrent cholestasis with normal gamma-glutamyl-transpeptidase activity. J Pediatr 1992; 121: 78–80.
  14. Clayton Robert J., Byler Disease : Fatal Familial Intrahepatic Cholestasis in an Amish Kindred, 10.1001/archpedi.1969.02100030114014
  15. Whitington Peter F., Whitington Gene L., Partial external diversion of bile for the treatment of intractable pruritus associated with intrahepatic cholestasis, 10.1016/0016-5085(88)90301-0
  16. Veyckemans F, Baele P, Guillaume JE Willems E Robert A, Clerbaux T. Hyperbilirubinemia does not interfere with hemoglobin saturation measured by pulse oximetry. Anesthesiology 1989; 70: 118–22.
  17. Silver MM, Bohn D, Shawn DH, et al. Association of pulmonary hypertension with congenital portal hypertension in a child. J Pediatr 1992; 120: 321–9.
  18. Gelman S, Femette L. Effects of anaesthetics on liver blood flow. In: Strunin L, Thomson S (Eds.). Baillière’s Clinical Anesthesiology. The Liver and Anaesthesia. London: Baillière Tindall, 1992; 729–50.
  19. Gelman S, Fowler KC, Smith LR. Liver circulation and function during isoflurane and halothane anesthesia. Anesthesiology 1984; 61: 726–30.
  20. Ahlgren I, Aronsen F, Bjorkman I, Wetterlin S. The hemodynamic effect of halothane in the normovolemic dog. Acta Anaesthesiol Scand 1978; 22: 83–92.
  21. Wark H, Earl J, Cooper M, Overton J. Halothane in children with chronic liver disease. Anaesth Intensive Care 1991; 19: 9–16.
  22. Philipps AJ, Brimacombe JR, Simpson DL. Anaesthetic induction with isoflurane or halothane. Anaesthesia 1988; 43: 927–9.
  23. Merin R, Bernard J-M, Doursout M-F, Cohen M, Chelly JE. Comparison of the effects of isoflurane and desflurane on cardiovascular dynamics and regional blood flow in the chronically instrumented dog. Anesthesiology 1991; 74: 568–72.
  24. Bernard J-M, Doursout M-F, Wouters P, Hartley C, Merin R, Chelly JE. Effects of sevoflurane and isoflurane on hepatic circulation in the chronically instrumented dog. Anesthesiology 1992; 77: 541–5.
  25. Patwardhan RV, Johnson RF, Hoyumpa A Jr, et al. Normal metabolism of morphine in cirrhosis. Gastroenterology 1981; 81: 1006–11.
  26. Bower S, Sear JW, Roy RC, Carter RF. Effects of different hepatic pathologies on disposition of alfentanil in anaesthetized patients. Br J Anaesth 1992; 68: 462–5.
  27. Krishna DR, Klotz U. Extrahepatic metabolism of drugs in humans. Clin Pharmacokinet 1994; 26: 144–60.
  28. Veroli P, O’Kelly B, Bertrand F, Trouvin JH, Farinotti R, Ecoffey C. Extrahepatic metabolism of propofol in man during the anhepatic phase of orthotopic liver transplantation. Br J Anaesth 1992; 68: 183–6.
  29. Janicki PK, James MFM, Erskine WAR. Propofol inhibits enzymatic degradation of alfentanil and sufentanil by isolated liver microsomesin vitro. Br J Anaesth 1992; 68: 311–2.
  30. Shafer SL, Stanski DR. Improving the clinical utility of anesthetic drug pharmacokinetics (Editorial). Anesthesiology 1992; 76: 327–30.
  31. Raoof AA, van Obbergh LJ, Verbeeck RK. Propofol pharmacokinetics in children with biliary atresia. Br J Anaesth 1995; 74: 46–9.
  32. Servin F, Desmonts JM, Haberer JP, Cockshott ID, Plummer GF, Farinotti R. Pharmacokinetics and protein binding of propofol in patients with cirrhosis. Anesthesiology 1988; 69: 887–91.
  33. Van de Velde M, Wouters PF, Marcus A, Flameng W, Van Aken H. Effects of propofol on hepatic and renal perfusion in chronically instrumented dogs. Anesth Analg 1994; 78: S451.
  34. Murray JM, Trinick TR. Hepatic function and indocyanine green clearance during and after prolonged anaesthesia with propofol. Br J Anaesth 1992; 69: 643–4.
  35. Pandele G, Chaux F, Salvadori C, Duvaldestin P. Thiopental pharmacokinetics in patients with cirrhosis. Anesthesiology 1983; 59: 123–6.
  36. Kay B. Ketamine. In: Kay B (Ed.). Total Intravenous Anesthesia. Amsterdam: Elsevier, 1991; 125–35.
  37. BEEM H., MANGER F. W., BOXTEL C., BENTEM N., Etomidate anaesthesia in patients with cirrhosis of the liver: pharmacokinetic data, 10.1111/j.1365-2044.1983.tb15181.x
  38. Davis PJ, Stiller R, Cook DR, Brandom BW, Davis JE, Scierka AM. Effects of cholestatic hepatic disease and chronic renal failure on alfentanil pharmacokinetics in children. Anesth Analg 1989; 68: 579–83.
  39. Haberer JP, Schoeffler P, Couderc E, Duvaldestin P. Fentanyl pharmacokinetics in anaesthetized patients with cirrhosis. Br J Anaesth 1982; 54: 1267–9.
  40. Chauvin M., Ferrier C., Haberer J. P., Spielvogel C., Lebrault C., Levron J. C., Duvaldestin P., Sufentanil Pharmacokinetics in Patients with Cirrhosis : , 10.1213/00000539-198901000-00001
  41. Egan TD, Lemmens HJM, Fiset P, et al. The pharmacokinetics of the new short-acting opioid remifentanil (GI87084B) in healthy adult male volunteers. Anesthesiology 1993; 79: 881–92.
  42. Shelly MP, Cory EP, Park GR Pharmacokinetics of morphine in two children before and after liver transplantation. Br J Anaesth 1986; 58: 1218–23.
  43. Priebe Hans-Joachim, Foëx Pierre, Isoflurane Causes Regional Myocardial Dysfunction in Dogs with Critical Coronary Artery Stenoses : , 10.1097/00000542-198703000-00005
  44. Ward S, Neill EAM. Pharmacokinetics of atracurium in acute liver failure (with acute renal failure). Br J Anaesth 1983; 55: 1169–72.
  45. Whittaker M. Plasma cholinesterase variants and the anaesthetist. Anaesthesia 1980; 35: 174–97.
  46. Duvaldestin P, Agoston S, Henzel E, Kersten UW, Desmonts JM. Pancuronium pharmacokinetics in patients with liver cirrhosis. Br J Anaesth 1978; 50: 1131–6.
  47. Lebrault C, Berger JL, D’Hollander AA, Gomeni R, Henzel D, Duvaldestin P. Pharmacokinetics and pharmacodynamics of vecuronium (ORG NC 45) in patients with cirrhosis. Anesthesiology 1985; 62: 601–5.
  48. Cook DR, Freeman JR, Lai AA, et al. Pharmacokinetics of mivacurium in normal patients and in those with hepatic or renal failure. Br J Anaesth 1992; 69: 580–5.
  49. Khalil M, D’Honneur G, Duvaldestin P, Slavov V, De Hys C, Gomeni R. Pharmacokinetics and pharmacodynamics of rocuronium in patients with cirrhosis. Anesthesiology 1994; 80: 1241–7.
  50. Tucker GT, Mather LE. Properties, absorption, and disposition of local anesthetic agents. In: Cousins MJ, Bridenbaugh PO (Eds.). Neural Blockade in Clinical Anesthesia and Management of Pain, 2nd ed. Philadelphia: Lippincott, 1988; 47–111.
  51. Nahata M. C., Powell D. A., Durrell D. E., Miller M. A., Acetaminophen accumulation in pediatric patients after repeated therapeutic doses, 10.1007/bf02395207
  52. Lindsley CB. Uses of nonsteroidal anti-inflammatory drugs in pediatrics. American Journal of Diseases in Children 1993; 147: 229–36.