Background: • Congenital portosystemic shunts (CPSS) are increasingly diagnosed in children and adults owing to high resolution imaging. • Their natural history is incompletely understood. • CPSS may be associated with life-threatening complications. • There are no established predictors of spontaneous closure. •Among patients in whom CPSS does not close spontaneously, is unclear which patients will develop complications, consequently which shunts require closure. Aim: To use preliminary data from 15/28 centers participating in the International Registry for Congenital Porto-Systemic Shunts (IRCPSS) to identify trends that might inform management decisions
McLin, V. ; Franchi-Abella, S ; Debray, D. ; Korff, S. ; Casotti, V. ; et. al. Congenital porto-systemic shunts in children: preliminary results from the IRCPSS.The International Liver Congress (EASL) (Genève, Suisse, du 10/04/2019 au 14/04/2019).