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Leiomyoma of the suprarenal gland in a child with ataxia-telangiectasia.

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Mouchet, F Ninane, J. Gosseye, Serge [UCL] Dumoulin, Christine [UCL] Bonnier, Christine Evrard, Philippe [UCL] Vermylen, Christiane [UCL] Scheiff, Jean-Marie [UCL] Cornu, Guy [UCL]

We report the occurrence of a leiomyoma of the suprarenal gland in a 10-year-old girl with ataxia-telangiectasia (A-T). Muscle cell tumors are very uncommon in this gland as they are in A-T. Possible reasons for developing nonhematologic tumors in this syndrome are reviewed. A defect in DNA repair mechanisms probably favors, in young children, the expression of tumors normally expected in the aged.

Document type Article de périodique (Journal article) – Article de recherche – Case Reports, Journal Article
Publication date 1991
Language Anglais
Journal information "Pediatric hematology and oncology" - Vol. 8, no. 3, p. 235-41 (1991)
Peer reviewed yes
issn 0888-0018
Publication status Publié
Affiliations UCL - (SLuc) Service de neurologie pédiatrique
UCL - MD/MNOP - Département de morphologie normale et pathologique
UCL - MD/GYPE - Département de gynécologie, d'obstétrique et de pédiatrie
MESH Subject Adrenal Gland Neoplasms - etiology - genetics - pathology ; Ataxia Telangiectasia - complications - genetics ; Child ; Female ; Hematologic Tests ; Humans ; Inversion, Chromosome ; Leiomyoma - etiology - genetics - pathology ; Neoplasm Staging ; Translocation, Genetic
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Bibliographic reference Mouchet, F ; Ninane, J. ; Gosseye, Serge ; Dumoulin, Christine ; Bonnier, Christine ; et. al. Leiomyoma of the suprarenal gland in a child with ataxia-telangiectasia.. In: Pediatric hematology and oncology, Vol. 8, no. 3, p. 235-41 (1991)
Permanent URL http://hdl.handle.net/2078.1/27208